Intimal sarcoma of the pulmonary artery presenting as pulmonary embolism

Authors

  • María Camila Plata Pontifical Javeriana University
  • Diana Lucía Rey Pontifical Javeriana University
  • Claudio Villaquirán Pontifical Javeriana University
  • Diego Rosselli Pontifical Javeriana University

DOI:

https://doi.org/10.17533/udea.iatreia.v30n3a10

Keywords:

diagnosis, differential, pulmonary artery, pulmonary embolism, sarcoma

Abstract

Los sarcomas de la arteria pulmonar son extremadamente raros; debido a su crecimiento lento y silencioso, el diagnóstico suele ser tardío y son de mal pronóstico. Presentamos el caso de una mujer de 33 años de edad con historia de disnea, dolor torácico y síncope. Una masa que obstruía el ventrículo derecho, el tronco pulmonar y la arteria pulmonar derecha llevó a la sospecha de embolismo pulmonar. 

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Author Biographies

María Camila Plata , Pontifical Javeriana University

Clinical Epidemiology and Biostatistics Department, Pontifical Javeriana University, Medical School, Bogotá, Colombia.

Diana Lucía Rey , Pontifical Javeriana University

Respiratory Diseases Unit, Internal Medicine Department, San Ignacio University Hospital, Pontifical Javeriana University, Medical School, Bogotá, Colombia.

 

Claudio Villaquirán, Pontifical Javeriana University

Respiratory Diseases Unit, Internal Medicine Department, San Ignacio University Hospital, Pontifical Javeriana University, Medical School, Bogotá, Colombia.

Diego Rosselli, Pontifical Javeriana University

Clinical Epidemiology and Biostatistics Department, Pontifical Javeriana University, Medical School, Bogotá, Colombia.

References

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(6.) Furest I, Marín M, Escribano P, Gómez MA, Cortinac J, Blanquer R. [Intimal sarcoma of the pulmonary artery: a rare cause of pulmonary hypertension]. Arch Bronconeumol. 2006 Mar;42(3):148-50. Spanish.

(7.) Yi CA, Lee KS, Choe YH, Han D, Kwon OJ, Kim S. Computed tomography in pulmonary artery sarcoma: distinguishing features from pulmonary embolic disease. J Comput Assist Tomogr. 2004 Jan- Feb;28(1):34-9.

(8.) Dias OM, Lombardi EM, Canzian M, Soares Júnior J, Vieira Lde O, Terra Filho M. 18F-fluorodeoxyglucose positron emission tomography as a noninvasive method for the diagnosis of primary pul- monary artery sarcoma. J Bras Pneumol. 2011 Nov-Dec;37(6):817-22. English, Portuguese.

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Published

2017-07-04

How to Cite

1.
Plata MC, Rey DL, Villaquirán C, Rosselli D. Intimal sarcoma of the pulmonary artery presenting as pulmonary embolism. Iatreia [Internet]. 2017 Jul. 4 [cited 2025 Feb. 8];30(3):340-3. Available from: https://revistas.udea.edu.co/index.php/iatreia/article/view/323641

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Case reports

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