Collapsing variant of focal segmental glomerulosclerosis in children

Authors

  • Jonh Fredy Nieto Ríos Hospital Pablo Tobón Uribe
  • Sandra Milena Brand Hospital Pablo Tobón Uribe
  • Lina María Serna Higuita Hospital Pablo Tobón Uribe
  • Luis Fernando Arias Universidad de Antioquia

DOI:

https://doi.org/10.17533/udea.iatreia.14323

Keywords:

Glomerulosclerosis, Focal Segmental, Nephrotic Syndrome, Kidney Failure, Chronic

Abstract

Focal segmental glomerulosclerosis (FSGS) collapsing variant refers to a renal lesion that may be idiopathic or associated to some factors, characterized by glomerular collapse leading to cortico-resistant nephrotic syndrome and chronic progressive renal failure. This glomerulopathy has been scarcely studied in children, but in this age group most cases are idiopathic. In this paper we present a report of 6 cases of collapsing variant of FSGS in children no associated to HIV, which were resistant to immunosuppressive management and with a high mortality

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Author Biographies

Jonh Fredy Nieto Ríos, Hospital Pablo Tobón Uribe

Nephrologist

Hospital Pablo Tobon Uribe

Sandra Milena Brand, Hospital Pablo Tobón Uribe

Pediatrics Nephrologist

Lina María Serna Higuita, Hospital Pablo Tobón Uribe

Pediatrics Nephrologist

Luis Fernando Arias, Universidad de Antioquia

Kidney Patologo

Published

2013-09-24

How to Cite

1.
Nieto Ríos JF, Brand SM, Serna Higuita LM, Arias LF. Collapsing variant of focal segmental glomerulosclerosis in children. Iatreia [Internet]. 2013 Sep. 24 [cited 2025 Dec. 5];26(4):Pág. 481-486. Available from: https://revistas.udea.edu.co/index.php/iatreia/article/view/14323

Issue

Section

Case reports

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